Advances in Clinical and Experimental Medicine

Title abbreviation: Adv Clin Exp Med
JCR Impact Factor (IF) – 1.736
5-Year Impact Factor – 2.135
Index Copernicus  – 168.52
MEiN – 70 pts

ISSN 1899–5276 (print)
ISSN 2451-2680 (online)
Periodicity – monthly

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Advances in Clinical and Experimental Medicine

2020, vol. 29, nr 2, February, p. 257–264

doi: 10.17219/acem/115238

Publication type: review article

Language: English

License: Creative Commons Attribution 3.0 Unported (CC BY 3.0)

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Pulmonary rehabilitation in interstitial lung diseases: A review of the literature

Krzysztof Wytrychowski1,A,B,C,D,F, Anna Hans-Wytrychowska2,A,B,D,E, Paweł Piesiak3,B,C,E, Marta Majewska-Pulsakowska4,A,B,C,D,E, Krystyna Rożek-Piechura5,E,F

1 Department and Clinic of Internal Medicine, Pneumonology and Allergology, Wroclaw Medical University, Poland

2 Department of Family Medicine, Wroclaw Medical University, Poland

3 Department and Clinic of Pulmonology and Lung Cancers, Wroclaw Medical University, Poland

4 Department and Division of Medical Rehabilitation, Wroclaw Medical University, Poland

5 Department of Rehabilitation in Internal Diseases, University School of Physical Education, Wrocław, Poland

Abstract

There are more than 200 different diseases classed as interstitial lung diseases (ILDs). For epidemiological and practical purposes, ILDs are classified into diseases of known and unknown etiology. The aim of this review is to evaluate our current knowledge about the efficacy and safety of pulmonary rehabilitation (PR) in patients with ILDs. Other issues, such as ILD pathogenesis, prevalence and comorbidity, are also elaborated in the review. Pulmonary rehabilitation is an important part of comprehensive care for patients with ILDs. In comparison to PR for patients with chronic pulmonary obstructive disease (COPD), the number of clinical studies concerning PR for patients with ILDs is small. The majority of trials have been performed in relatively small groups of patients. The principles of PR in this group of patients are the same as for patients with COPD. Exercise-induced desaturation is frequently observed during PR, which is the main source of complications in patients with ILDs. Major differences between ILD and COPD patients include poorer exercise tolerance and faster development of respiratory failure in patients with ILDs.

Key words

pulmonary rehabilitation, airway management, interstitial lung diseases

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