Advances in Clinical and Experimental Medicine

Title abbreviation: Adv Clin Exp Med
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ISSN 1899–5276 (print)
ISSN 2451-2680 (online)
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Advances in Clinical and Experimental Medicine

2010, vol. 19, nr 6, November-December, p. 765–769

Publication type: review article

Language: English

Facial Features in Binder’s Syndrome – Review of the Literature

Cechy twarzy w zespole Bindera – przegląd piśmiennictwa

Anna Paradowska1,, Anna Znamirowska-Bajowska1,, Janina Szeląg1,

1 Department of Facial Abnormalities, Department of Maxillofacial Orthopedics and Orthodontics, Wroclaw Medical University, Wroclaw, Poland

Abstract

Binder’s syndrome develops in the first trimester of pregnancy and has characteristic effects on the facial features. Those effects are: arhinoid face, intermaxillary hypoplasia (associated with malocclusion), abnormal position of the nasal bones, nasal mucosa atrophy, anterior nasal spine agenesis and (in most cases) a lack of frontal sinuses. Other deformities, as well as mental retardation, are also possible. Due to the clinical appearance, patients require surgical and orthodontic treatment. The main surgery performed in these patients is nose reconstruction with bone or cartilage grafts. Usually patients require more than one surgical procedure due to graft resorbtion and an unsatisfactory appearance. Orthodontic treatment is based on Class III treatment (pseudo-mesio-occlusion) and relieving dental crowding. The treatment of malocclusion may require combined orthodontic and surgical treatment. In younger patients maxillary protraction with rapid palatal expansion could be an adequate approach.

Streszczenie

Zespół Bindera jest wynikiem zaburzenia w tworzeniu się nosa i formuje się w trzecim miesiącu ciąży. Charakteryzuje go wiele cech, dotyczących głównie twarzy. Są to: pozorny brak nosa, hipoplazja szczęki (z towarzyszącymi wadami zgryzu), nieprawidłowe ustawienie kości nosa, atrofia błony śluzowej nosa, zredukowany przedni grzebień nosa i (w większości przypadków) brak zatok przednich. Inne zaburzenia rozwojowe, podobnie jak opóźnienie umysłowe, są także możliwe. Ze względu na wygląd kliniczny pacjent wymaga leczenia chirurgicznego i ortodontycznego. Wykonuje się zabiegi rekonstrukcji nosa z użyciem wszczepów kostnych bądź chrzęstnych. Pacjent zwykle wymaga więcej niż jednego zabiegu chirurgicznego, co jest związane z resorpcją wszczepu i niesatysfakcjonującym wyglądem. Leczenie ortodontyczne obejmuje leczenie wady klasy III (przodozgryz rzekomy) i likwidację stłoczeń. Leczenie może wymagać skojarzonego leczenia ortodontycznego i chirurgicznego. U młodszych pacjentów można zastosować protrakcję z poszerzeniem szczęki.

Key words

Binder’s syndrome, maxillofacial hypoplasia, pseudoprognathism

Słowa kluczowe

zespół Bindera, hipoplazja twarzowo-szczękowa, przodozgryz rzekomy

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